Document Type

Article

Publication Date

11-14-2022

Abstract

Masses occupying the retrolabyrinthine space are uncommon and most often represent paragangliomas, choroid plexus papilloma, endolymphatic sac tumors (ELSTs) or distant metastasis. ELSTs are rare, locally invasive tumors of the inner ear, with less than 300 cases reported in the literature. ELSTs are associated with von-Hippel Lindau (VHL) disease. Patients diagnosed with an ELST should undergo genetic testing for VHL disease, and individuals with confirmed VHL disease should be screened for ELST(s).

Comments

This article was published in Ear, Nose and Throat Journal.

The published version is available at https://doi.org/10.1177/01455613221139408.

Copyright © 2022 The Author(s). CC BY-NC 4.0.

Publication Title

Ear, Nose, & Throat Journal

PubMed ID

36377117

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